HEMOPHILIA ETIOLOGY DEFINATION TYPES CLINICAL MANIFESTATION DIAGNOSIS MANAGMENT ~ Medical diseases and trems ,symptoms causes TREATMENT

Medieducator.com

HEMOPHILIA ETIOLOGY DEFINATION TYPES CLINICAL MANIFESTATION DIAGNOSIS MANAGMENT



HEMOPHILIA

        Hemophilia is a sex link inheritance disorder characterised by prolong bleeding after a cut or injury .

It also known as "Royal disorder".

ETIOLOGY 

      It is a sex link inheritance disorder .

     The defective gene of hemophilia are found upon X chromosome.

TYPES

1. HEMOPHILIA A → [CLASSICAL HEMOPHILIA]

                   * Most common type occur due to the deficiency of factor number VIII .

2. HEMOPHILIA B [CHRISMIS DISEASE]→

            * It occur due to the deficiency of factor IX .

3. HEMOPHILIA C

        * It occur due to the deficiency of factor XI .

CLINICAL MANIFESTATION

   * Prolong bleeding after a cut or injury .

   * epistaxis .

   * Risk of intra cranial hemorrhage .

   * joint bleeding risk of joint damage .

DIAGNOSIS 

      *   Bleeding time  Normal  .

      *  Clotting time increase .

      * APTT Increased [diagnosis of choice ]

MANAGEMENT 

   Advise → *  Avoid himself from injury 

                    * Avoid the out door game .

                    * If injury occur then tight bandage has been done and ice application done.

EMERGENCY MANAGEMENT  →

                                                  *   Administer FFP.

                                                  * Administer  Desmopressin  - it is drug of choice.

                                                  * Administer concentrat factor VIII /IX .


1 comment:

  1. I quite like the many written content, I've got to declare my spouse and i loved, My spouse and i would really like more details relating to this specific, mainly because it is quite wonderful., Thanks a lot with regards to disclosing. Malaria Treatment

    ReplyDelete